Rare manifestation of limited scleroderma: only facial skin involvement

Sclerodermais a multisystem autoimmune disease in which there is increased fibroblast activity resulting in abnormal growth of connective tissue. Systemic sclerosis is classified into two main types: Diffuse cutaneous and limited cutaneous scleroderma. Commonest presentations of limited scleroderma were Calcinosis, Raynaud's phenomenon, oesophageal dysmotility, Sclerodactyly, Telangiectasia and only facial skin manifestation is very rare presentation. We are presenting a case report of rare involvement of facial skin only as an initial manifestation of limited scleroderma.