Perioperative anaesthesia care in a child with hereditary spherocytosis for laparoscopic splenectomy

Hereditary spherocytosis (HS) is a familial haemolyticdisorder characterizedby formation of abnormal red blood cells with fragile cell walls causing anaemia, jaundice, splenomegaly and gallstone formation. Most children have a mild disease and hencedo not require splenectomy, mainly reserved for a severe disease or in patients with symptomatic gall stone disease. The anaesthetic management of hereditary spherocytosis mainly depends upon the degree of haemolysis and severity of anaemia.We reportanaesthetic management in a case of HS with splenomegaly for elective laparoscopic SOS open splenectomy.