Hydatid cysts are due to parasitic infection caused by cestode tape worm Echinococcus. Hydatid cyst most commonly involves the liver and lung. Involvement of kidney and retroperitoneum without involvement of other major organ are much less common. We reported a recent case of hydatid cyst involving both kidney and retroperitoneum. This case was diagnosed by radiological study followed by serology and lastly by laparotomy. The case was treated by surgical removal of the cysts combined with chemotherapy before and after surgery.