Imaging in bronchopulmonary sequestration

Bronchopulmonary Sequestration is a rare congenital malformation of lower respiratory tract that lacks normal communication with the tracheobronchial tree. In 1977, Huber stated that aberrant arterial supply of sequestered lung could be encountered. The term pulmonary sequestration was first used in 1946 by Pryce. It was also termed as bronchoarterial malinosculation by clements in 1987. It is a non functional mass composed of dysplastaic lung parenchyma, embryologically detached from the tracheobronchial tree and receiving its own blood supply from a systemic artery, usually 75% from thoracic or abdominal aorta and 25% of sequestrations receive their blood flow from the subclavian, intercostals, pulmonary, pericardiophrenic, innominate, internal mammary, celiac, splenic or renal artery. The venous drainage is variable (1) computed Tomography, magnetic resonance angiography are able to demonstrate the aberrant arterial vessel feeding the sequestration. The blood supply of 75% of pulmonary sequestrations is derived from the thoracicabdominal aorta. The remaining 25% of sequestrations receive their blood flow from the subclavian, intercostal, pulmonary, pericardiophrenic, innominate, internal mammary, celiac, splenic, or renal arteries.